本文選題：Dyke-Davidoff-Masson綜合征　切入點(diǎn)：單側(cè)大腦萎縮　出處：《廣東醫(yī)學(xué)》2017年S1期 　論文類型：期刊論文

【摘要】：目的探討Dyke-Davidoff-Masson(DDM)綜合征的臨床及影像學(xué)特征,提高對(duì)DDM綜合征的認(rèn)識(shí)并減少漏診及誤診。方法回顧性分析經(jīng)CT及MRI診斷的5例DDM綜合征患者的臨床及影像學(xué)資料,總結(jié)其影像學(xué)診斷依據(jù)。結(jié)果 5例患者中男2例,女3例,發(fā)病年齡9~55歲,平均(32±15)歲。臨床表現(xiàn)為癲癇發(fā)作,面部不對(duì)稱及對(duì)側(cè)肢體無力。影像學(xué)均表現(xiàn)為左側(cè)大腦萎縮,患側(cè)側(cè)腦室擴(kuò)大,中線結(jié)構(gòu)向患側(cè)偏移,患側(cè)顱窩縮小,顱骨增厚。1例合并患側(cè)丘腦、豆?fàn)詈思按竽X腳萎縮,1例合并腦實(shí)質(zhì)軟化灶,1例合并腦穿通畸形囊腫。結(jié)論 DDM綜合征具有典型的影像學(xué)表現(xiàn),結(jié)合臨床表現(xiàn)可以作出診斷。
[Abstract]:Objective to investigate the clinical and imaging features of Dyke-Davidoff-Masson DDM syndrome, to improve the understanding of DDM syndrome and to reduce misdiagnosis and misdiagnosis. Methods the clinical and imaging data of 5 patients with DDM syndrome diagnosed by CT and MRI were analyzed retrospectively. Results among the 5 patients, 2 were male and 3 were female. The onset age was 9 to 55 years (mean 32 鹵15) years. The clinical manifestations were epileptic seizures, facial asymmetry and contralateral limb weakness. The ventriculus of the affected side was enlarged, the midline structure shifted to the affected side, the cranial fossa was reduced, and the skull was thickened in 1 cases with the thalamus of the affected side. Lentiform nucleus and atrophy of the cerebral feet were found in 1 case with cerebral parenchymatomalacia and 1 case with cerebral perforation malformation cyst. Conclusion DDM syndrome has typical imaging features and can be diagnosed with clinical manifestations.
【作者單位】： 中山市東升醫(yī)院影像科;
【分類號(hào)】：R445.2;R742;R816.1
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本文編號(hào)：1615466