【摘要】：目的探討平山病的臨床、神經(jīng)電生理與頸椎磁共振特點(diǎn)。方法收集11例平山病青少年患者資料,分析其臨床、神經(jīng)電生理與頸椎磁共振特征,總結(jié)規(guī)律。結(jié)果 11例患者發(fā)病年齡15~17歲,均隱匿起病,均以單側(cè)上肢遠(yuǎn)端力弱、肌肉萎縮為主要臨床表現(xiàn),體格檢查均可見(jiàn)大小魚(yú)際肌、骨間肌為主肌群不同程度肌力下降、肌萎縮伴肌束震顫。神經(jīng)傳導(dǎo)速度檢查可見(jiàn)尺神經(jīng)及正中神經(jīng)CMAP波幅降低,針電極肌電圖可見(jiàn)運(yùn)動(dòng)單位時(shí)限增寬,波幅增高,并可見(jiàn)纖顫電位、正銳波等自發(fā)電位。頸椎磁共振可見(jiàn)下段頸髓受壓變細(xì)并局部萎縮,過(guò)屈位磁共振可見(jiàn)迂曲條狀血管流空影。結(jié)論平山病具有其獨(dú)特的臨床表現(xiàn),需重視其診斷與早期治療,神經(jīng)電生理及頸椎磁共振檢查尤其過(guò)屈位磁共振對(duì)于該病診斷具有重要價(jià)值。
[Abstract]:Objective to investigate the clinical, neurophysiological and magnetic resonance characteristics of Pingshan disease. Methods the data of 11 young patients with Pingshan disease were collected, and the clinical, electrophysiological and magnetic resonance characteristics of cervical vertebrae were analyzed. Results the onset age of 11 patients was 15 ~ 17 years old. All the patients had occult onset. The main clinical manifestations were weak distal strength of unilateral upper limb and muscular atrophy. The physical examination showed that the size of thenar muscles and interosseous muscles decreased in different degrees. Muscle atrophy with muscle bundle tremor. The CMAP amplitude of ulnar nerve and median nerve was decreased in nerve conduction velocity examination, and the motor unit duration widened, amplitude increased, fibrillation potential and positive sharp wave spontaneous potential were observed in needle electrode electromyography. Cervical MRI showed that the lower cervical spinal cord was compressed and local atrophy, and the tortuous vascular flow void could be seen on overflexion MRI. Conclusion Pingshan disease has its unique clinical manifestations, so it is necessary to pay attention to the diagnosis and early treatment of Pingshan disease. The neuroelectrophysiology and magnetic resonance imaging of cervical vertebrae are of great value in the diagnosis of the disease.
【作者單位】： 河南省人民醫(yī)院神經(jīng)內(nèi)科;
【分類(lèi)號(hào)】：R741
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本文編號(hào)：2292531