本文選題：血管瘤　切入點：氣管　出處：《中國呼吸與危重監(jiān)護雜志》2017年04期 　論文類型：期刊論文

【摘要】：目的探討氣管血管瘤的臨床表現(xiàn)、診斷、鑒別診斷、病理學(xué)特征、治療及預(yù)后,提高對該病的診療水平。方法回顧性分析四川大學(xué)華西醫(yī)院收治的1例氣管血管瘤患者的臨床資料并進行相關(guān)文獻(xiàn)復(fù)習(xí)。以"氣道血管瘤"或"支氣管血管瘤"為檢索詞檢索中國期刊網(wǎng)全文數(shù)據(jù)庫、萬方數(shù)據(jù)庫及維普數(shù)據(jù)庫,以"Trachea"OR"Bronchus"AND"Hemangioma"為檢索詞檢索Pub Med、Ovid Medline及Embase數(shù)據(jù)庫,檢索時間為1976年1月1日至2016年10月31日。結(jié)果患者為32歲男性,主訴為"背痛、咯血10~+d"。其胸部增強CT提示食管壁全程增厚,食管管腔變窄,纖維支氣管鏡顯示氣管及雙側(cè)支氣管廣泛血管瘤樣改變,胃鏡檢查提示食管靜脈瘤�；颊邭夤軆�(nèi)病變廣泛,但經(jīng)內(nèi)科保守治療后,咯血癥狀明顯緩解,隨訪至今病情未復(fù)發(fā)。經(jīng)上述數(shù)據(jù)庫檢索,有34篇文獻(xiàn)36例患者明確診斷為氣管血管瘤并且具有相關(guān)臨床資料。其臨床癥狀主要為反復(fù)咯血,影像表現(xiàn)不具有特征性,組織病理學(xué)表現(xiàn)為擴張、薄壁、管腔大小不一的血管或增生的毛細(xì)血管,免疫組織化學(xué)染色顯示血管內(nèi)皮細(xì)胞特異性CD34及Ⅷ因子陽性。結(jié)論血管瘤是一種常發(fā)生于嬰兒及兒童頭頸部的良性腫瘤,其在成人氣管、支氣管內(nèi)極其罕見。病因尚不清楚。臨床及影像表現(xiàn)不具有特征性,與淋巴管瘤易混淆。確診需依賴組織病理學(xué)檢查,纖維支氣管鏡及CT胸部血管三維重建成像在整個診治過程中起重要作用。氣管血管瘤的預(yù)后較好。
[Abstract]:Objective to investigate the clinical manifestations, diagnosis, differential diagnosis, pathological features, treatment and prognosis of trachea hemangioma. Methods the clinical data of a case of trachea hemangioma treated in Huaxi Hospital of Sichuan University were analyzed retrospectively and the related literatures were reviewed. "Airway hemangioma" or "bronchial hemangioma" In order to search the full text database of Chinese periodical network, Wanfang database and WIP database were used to search Pub MedOvid Medline and Embase database with "Trachea" OR "Bronchus" "AND" Hemangioma as the key words. The retrieval time was from January 1st 1976 to October 31st 2016. Results the patient was 32 years old male and the main complaint was "back pain". Hemoptysis 10 ~ d ". Chest enhanced CT showed that the wall of the esophagus became thicker, the esophageal lumen became narrower, the fiberoptic bronchoscopy showed extensive hemangiomatous changes of trachea and bilateral bronchus, and the gastroscopy showed that the esophageal vein tumor had a wide range of intratracheal lesions. However, after conservative medical treatment, hemoptysis symptoms were obviously relieved, and no recurrence was found after follow-up. Thirty-six patients with trachea hemangioma were diagnosed in 34 literature and had related clinical data. The clinical symptoms were mainly recurrent hemoptysis, the imaging manifestations were not characteristic, the histopathological manifestations were dilatation and thin-walled. Immunohistochemical staining showed that vascular endothelial cell specific CD34 and factor 鈪，

本文編號：1573780