本文選題：常染色體隱性多囊性腎病　切入點：磁共振成像　出處：《中國醫(yī)學影像技術(shù)》2017年02期

【摘要】：目的觀察嬰兒及少兒型常染色體隱性多囊性腎病(ARPKD)的CT、MRI表現(xiàn)。方法回顧性分析11例嬰兒及少兒型ARPKD患者腹部CT及MRI上肝葉比例、雙腎體積改變以及膽管與腎臟囊樣病灶的表現(xiàn)。結(jié)果 11例嬰兒及少兒型ARPKD患者中,5例(5/11,45.45%)肝葉比例失調(diào)。5例(5/11,45.45%)中央?yún)^(qū)域肝內(nèi)膽管以梭形擴張為主、3例(3/11,27.27%)肝邊緣部膽管擴張明顯、3例(3/11,27.27%)沿門靜脈周圍可見多發(fā)囊樣灶。2例(2/11,18.18%)腎臟體積增大。8例(8/11,72.73%)雙腎髓質(zhì)可見多發(fā)小囊樣灶、3例(3/11,27.27%)雙腎皮髓質(zhì)多發(fā)囊腫。8例(8/11,72.73%)門靜脈增粗、脾大。2例(2/11,18.18%)腹部可見多發(fā)腫大淋巴結(jié)。5例(5/11,45.45%)MR平掃T1WI顯示雙腎皮髓質(zhì)分界不清。結(jié)論嬰兒或少兒型ARPKD以肝膽改變?yōu)橹?特征性CT及MRI表現(xiàn)為肝葉比例與腎臟體積的改變合并膽管擴張及雙腎囊樣灶。
[Abstract]:Objective to observe the CT MRI findings of autosomal recessive polycystic nephropathy (ARPKD) in infants and children.Methods the ratio of upper lobe of abdomen CT and MRI, the changes of bilateral renal volume and cystic lesions of bile duct and kidney in 11 cases of infantile and juvenile ARPKD were analyzed retrospectively.緇撴灉 11渚嬪┐鍎垮強灝戝効鍨婣RPKD鎮(zhèn)ｈ，

本文編號：1713984