永存第五對(duì)主動(dòng)脈弓胚胎發(fā)育及臨床診療的研究進(jìn)展
發(fā)布時(shí)間:2018-07-11 21:56
本文選題:胚胎發(fā)育 + 流行病學(xué)現(xiàn)狀; 參考:《中國(guó)循證兒科雜志》2017年04期
【摘要】:正永存第五對(duì)主動(dòng)脈弓(PFAA)是一類極其罕見的先天性心血管畸形,系胚胎發(fā)育過程中第五對(duì)主動(dòng)脈弓發(fā)育異常所致的一類先天性主動(dòng)脈弓畸形~([1])。自1969年Van Praagh~([2])等報(bào)道尸檢發(fā)現(xiàn)PFAA后,世界各地學(xué)者陸續(xù)對(duì)PFAA進(jìn)行了病例和病例系列報(bào)告。本文就PFAA的胚胎發(fā)育過程及其臨床診斷和治療簡(jiǎn)要綜述。1流行病學(xué)現(xiàn)狀PFAA發(fā)病率極低,Gerlis~([3])等發(fā)現(xiàn)2 000例先天性心
[Abstract]:The fifth pair of aortic arch (PFAA) is a very rare congenital cardiovascular malformation. It is a kind of congenital aortic arch malformation caused by abnormal development of the fifth pair of aortic arch during embryonic development. Since Van Praagh2 et al reported the discovery of PFAA in 1969, scholars from all over the world have reported PFAA cases and case series one after another. A brief review of the embryonic development process and its clinical diagnosis and treatment of PFAA. 1 Epidemiology of PFAA with extremely low incidence of Gerlis ~ ([3]) in the diagnosis of 2 000 cases of congenital heart disease
【作者單位】: 重慶醫(yī)科大學(xué)附屬兒童醫(yī)院心內(nèi)科兒童發(fā)育疾病研究教育部重點(diǎn)實(shí)驗(yàn)室兒童發(fā)育重大疾病治療與預(yù)防國(guó)際科技總基地兒童感染免疫重慶市重點(diǎn)實(shí)驗(yàn)室;
【基金】:國(guó)家自然科學(xué)基金項(xiàng)目:81301300 重慶市科學(xué)技術(shù)委員會(huì)社會(huì)事業(yè)與民生保障科技創(chuàng)新專項(xiàng):cstc2016shmszx130009
【分類號(hào)】:R725.4
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本文編號(hào):2116447
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